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Proximal Interruption of the Pulmonary Artery

Williams, Eric A. MD*; Cox, Chad MD; Chung, Jonathan H. MD; Grage, Rolf A. MD*; Rojas, Carlos A. MD*

doi: 10.1097/RTI.0000000000000373
Review Articles

Proximal interruption of the pulmonary artery (PIPA) is an uncommon developmental anomaly resulting in underdevelopment of the proximal portion of the pulmonary artery with preservation of the intrapulmonary segments. Clinical presentation ranges between an asymptomatic incidental finding to massive hemoptysis. When findings suggestive of PIPA are present radiographically, the diagnosis of PIPA can be definitively diagnosed with computed tomography or magnetic resonance pulmonary angiography. Other imaging modalities, such as nuclear perfusion scan and catheter angiography can help in the diagnosis.

*Division of Thoracic/Cardiac Radiology, Mayo Clinic, Jacksonville

Department of Radiology, University of South Florida Health, Tampa, FL

Department of Thoracic Radiology, University of Chicago Medical Center, Chicago, IL

The authors declare no conflicts of interest.

Correspondence to: Carlos A. Rojas, MD, Division of Thoracic/Cardiac Radiology, Mayo Clinic, 4500 San Pablo Rd., Jacksonville, FL 32224 (e-mail:

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