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Pheochromocytoma: “The Great Mimic”: Thrombosis of Portal Vein and Splenic Vessels as First Presentation of Pheochromocytoma

Petidis, Konstantinos MD; Douma, Stella MD; Doumas, Michael MD; Papaefthimiou, Panagiota MD; Kartali, Nikoletta MD; Vogiatzis, Konstantinos MD; Zamboulis, Chrysanthos MD

doi: 10.1097/TEN.0b013e318175d1d6
Case Report
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Pheochromocytoma is a tumor of the adrenal medulla that secretes catecholamines (noradrenaline and adrenaline). The clinical presentation is characterized by paroxysmal hypertension, tachycardia, headache, and sweating. Pheochromocytoma is associated with neurofibromatosis type 1. We report the case of a woman with neurofibromatosis type 1 and bilateral adrenal pheochromocytomas who presented with thrombosis of the portal vein, thrombocytosis, hepatic infarct, and stenosis of celiac artery. To our knowledge this is the first report of this constellation of findings as the presenting clinical picture of pheochromocytoma.

From the Second Propedeutic Department of Internal Medicine, Aristotle University of Thessaloniki, Thessaloniki, Greece.

Reprints: Konstantinos Petidis, MD, 88. Markou Botsari St., 58144 Thessaloniki, Greece. E-mail: petidisk@med.auth.gr.

© 2008 Lippincott Williams & Wilkins, Inc.