Case ReportINTRAVENOUS IMMUNOGLOBULIN IN THE TREATMENT OF JUVENILE RETINITIS PIGMENTOSA–ASSOCIATED CYSTOID MACULAR EDEMA AND UVEITISEdiriwickrema, Lilangi S. MD*; Chhadva, Priyanka MD†; Rodger, Damien C. MD, PhD*; Ameri, Hossein MD, PhD*; Rao, Narsing A. MD*Author Information *Department of Ophthalmology, Keck School of Medicine, University of Southern California, Los Angeles, California; and †Department of Ophthalmology, Miller School of Medicine, University of Miami, Miami, Florida. Reprint requests: Hossein Ameri, MD, PhD, 1450 San Pablo Street, Los Angeles, CA 90033; e-mail: email@example.com None of the authors has any financial/conflicting interests to disclose. Retinal Cases & Brief Reports: Summer 2018 - Volume 12 - Issue 3 - p 242-246 doi: 10.1097/ICB.0000000000000478 Buy Metrics AbstractIn Brief Purpose: To evaluate the efficacy of intravenous immunoglobulin in the treatment of cystoid macular edema and uveitis caused by juvenile retinitis pigmentosa in a woman interested in planning a pregnancy. Methods: Descriptive case report. A 25-year-old woman with retinitis pigmentosa presented with decreased visual acuity, interested in a second opinion. Results: Intravenous immunoglobulin therapy was begun at 2-week intervals. Visual acuity improved from 20/100 to 20/70 by 6 weeks, where it stabilized for the remaining year. Serial optical coherence tomography imaging revealed marked improvement in cystoid macular edema after 2 treatments of intravenous immunoglobulin at 2 weeks of follow-up, with complete resolution noted at 4 months, a finding that persisted at 1 year of follow-up. Conclusion: Our findings support the use of intravenous immunoglobulin as a therapeutic option for the resolution of cystoid macular edema and management of uveitis secondary to juvenile retinitis pigmentosa. Cystoid macular edema can cause central vision loss in patients with retinitis pigmentosa. Cases that are recalcitrant to traditional treatment or manifest in peripartum women can present as a therapeutic dilemma. The authors propose using intravenous immunoglobulin, which resulted in successful treatment of our patient with juvenile retinitis pigmentosa and uveitis.