Case ReportCAVERNOUS HEMANGIOMA ASSOCIATED WITH RETINAL MACROVESSELSBruè, Claudia MD*†‡; Vance, Sushma K MD*†; Yannuzzi, Lawrence A MD*†; Freund, K Bailey MD*†Author Information From the *Vitreous-Retina-Macula Consultants of New York, New York, New York; †LuEsther T. Mertz Retinal Research Center, Manhattan Eye, Ear, and Throat Hospital, New York, New York; and ‡Ophthalmology, Department of Neuroscience, University Politecnica of Marche, Ancona, Italy. Supported in part by The Macula Foundation, Inc., New York, NY. The authors have no financial interest. Reprint requests: K. Bailey Freund, MD, Vitreous, Retina, Macula Consultants of New York, 460 Park Avenue, 5th Floor, New York, NY 10022; e-mail: [email protected] Retinal Cases & Brief Reports: Fall 2011 - Volume 5 - Issue 4 - p 323-325 doi: 10.1097/ICB.0b013e3181f66bca Buy Metrics AbstractIn Brief Purpose: The purpose of this study was to report two unusual cases of retinal cavernous hemangiomas in conjunction with retinal macrovessels. Methods: Observational case study. Two patients with unilateral retinal cavernous hemangiomas and no signs or symptoms of systemic disease were evaluated with full ophthalmic examination and underwent fundus photography and fluorescein angiography. Results: Patient 1 had 20/20 visual acuity bilaterally and a normal funduscopic examination of the right eye. The left eye showed diffuse clusters of saccular aneurysms associated with a dilated superotemporal venous arcade that crossed the horizontal raphe temporally. Patient 2 had 20/30 visual acuity in the right eye and 20/20 visual acuity in the left eye. Funduscopic examination of the left eye was normal, but the right eye demonstrated multiple clusters of saccular dilations along the course of a dilated inferior retinal vein that crossed the horizontal raphe temporally. On fluorescein angiography, both patients had fluid–erythrocyte levels within the saccular aneurysms and areas of capillary nonperfusion anterior to the tumor. Conclusion: Retinal cavernous hemangioma is a rare hamartoma that is typically isolated. However, it may be associated with other major abnormalities of the retinal vascular pattern. The authors describe two unique cases of a retinal cavernous hemangioma in conjunction with a retinal macrovessel. Retinal cavernous hemangioma is a rare, benign, vascular tumor composed of an intraretinal cluster of saccular aneurysms of venous origin. This tumor usually occurs as an isolated finding in an otherwise normal appearing fundus. To the best of our knowledge, this is the first report describing cavernous hemangioma associated with retinal macrovessels. © 2011 Ophthalmic Communications Society, Inc.