Secondary Logo

Institutional members access full text with Ovid®

Share this article on:

Stepping Activity in Children With Congenital Myotonic Dystrophy

Hayes, Heather A., DPT, PhD; Dibella, Deanna, PT; Crockett, Rebecca, BS; Dixon, Melissa, PhD; Butterfield, Russel J., MD, PhD; Johnson, Nicholas E., MD

doi: 10.1097/PEP.0000000000000537
RESEARCH REPORTS

Purpose: The purpose of this study was to investigate the physical activity levels in children with congenital myotonic dystrophy (CDM), and to examine whether patient clinical and functional characteristics correlated to physical activity.

Methods: Twenty-five children with CDM were assessed on functional measures, clinical measures, and physical activity levels.

Results: Results support that children with CDM spend the majority of their time inactive. There was a negative correlation between inactivity and cytosine-thymine-guanine repeats, suggesting increased inactivity with increased CDM severity. Age, body mass index, and lean muscle mass may be factors influencing activity levels.

Conclusions: Children in this study received one-third the recommended steps per day. The number of steps per day is not correlated with clinical measures.

The purpose of this study was to investigate the physical activity levels in children with congenital myotonic dystrophy and to examine whether patient clinical and functional characteristics correlated to physical activity.

Department of Physical Therapy and Athletic Training (Dr Hayes) and Department of Neurology (Mss Dibella and Crockett and Drs Dixon, Butterfield, and Johnson), University of Utah, Salt Lake City, Utah.

Correspondence: Heather A. Hayes, DPT, PhD, Department of Physical Therapy and Athletic Training, University of Utah, 520 Wakara Way, Ste 120, Salt Lake City, UT 84108 (heather.hayes@hsc.utah.edu).

Grant Support: NIH (1K23NS091511-01), The Muscular Dystrophy Association, and Valerion Therapeutics.

The authors declare no conflicts of interest.

Copyright © 2018 Academy of Pediatric Physical Therapy of the American Physical Therapy Association