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Orbital Myxofibrosarcoma

Case Report and Review of Literature

Clair, Brandon C., M.D.*; Salloum, George, M.D.; Carruth, Bryant P., M.D.; Bersani, Thomas A., M.D.; Hill, Robert H. III, M.D.

Ophthalmic Plastic & Reconstructive Surgery: November/December 2018 - Volume 34 - Issue 6 - p e180–e182
doi: 10.1097/IOP.0000000000001219
Case Reports

Myxofibrosarcoma is rarely found in the orbit, let alone as a primary orbital tumor. With this having only been previously reported 5 times in the literature, there is a very limited understanding of its presentation and course. Typical management involves surgical excision with or without postoperative radiotherapy. Low-grade malignancy, although rare to metastasize, still has a high rate of local recurrence and with each recurrence increases the risk of metastatic potential. With this in mind, analysis of each case is critical in better understanding the disease, and this case adds to the current literature.

Myxofibrosarcoma (MFS) is extremely rare to find isolated to the orbit and with the definition of MFS having evolved, in conjunction with potentially poor survivability, analysis of each case is crucial to enhancing patient outcomes.

*Department of Ophthalmology, State University of New York at the University of Buffalo, Buffalo, New York, U.S.A.

Department of Ophthalmology, State University of New York Upstate Medical Center, Syracuse, New York, U.S.A.

Accepted for publication July 17, 2018.

The authors have no financial or conflicts of interest to disclose.

Presented at American Society of Ophthalmic Plastic and Reconstructive Surgery Fall Meeting, November 12-13, 2015, Las Vegas, NV, U.S.A.

Address correspondence and reprint requests to George Salloum, M.D., Center For Vision Care, 550 Harrison St. Suite L, Syracuse, NY 13202. E-mail:

© 2018 by The American Society of Ophthalmic Plastic and Reconstructive Surgery, Inc., All rights reserved.