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A Case Report of Sturge-Weber Syndrome With Gelastic Seizures

Wang, Fei MMed*; Gui, Songbai MD

doi: 10.1097/WNQ.0000000000000023
Case Report

Sturge-Weber syndrome (SWS) is characterized by the association of a facial capillary malformation with a vascular malformation of the eye, and/or vascular malformation of the brain. We report a case of 7-year-old boy who presented with a deep purple nevus of 5×7 cm on left side of the face since birth and gelastic seizures. Clinically, gelastic episodes were diagnosed secondary to SWS that improved with aggressive seizure management and low-dose aspirin use. We have attempted to identify the pathophysiology of the rare episodes in SWS. The case report underlines that the epileptic phenomena of the SWS may manifest with gelastic seizures and need correct identification and appropriate response for optimal management by doctors.

*Beijing Neurosurgical Institute

The Neurosurgical Department of Beijing Tiantan Hospital, Capital Medical University, Beijing, China

The authors declare no conflict of interest.

Reprints: Songbai Gui, MD, The Neurosurgical Department of Beijing Tiantan Hospital, Capital Medical University, 100050 Beijing, China (e-mail: guisongbai@yeah.net).

Copyright © 2015 Wolters Kluwer Health, Inc. All rights reserved.