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Giant Vulvar Lymphangioma Circumscriptum Mimicking Vulvar Tumor: A Case Report and Literature Review

Ghaemmaghami, Fatemeh MD1,2; Zarchi, Mojgan Karimi MD1,3

Journal of Lower Genital Tract Disease: October 2007 - Volume 11 - Issue 4 - p 281-283
doi: 10.1097/LGT.0b013e31815706e5
Case Reports

Background: Lymphangioma circumscriptum (LC) is a benign dilation of lymph channels localized to the skin and subcutaneous tissues. Primary vulvar involvement is very rare, with only 34 cases reported.

Case: A 17-year-old girl presented with pain and an 18-cm mass of the right labium majus that started 4 years earlier. She underwent wide local excision, and histological examination showed multiple dilated vascular channels in papillary dermis with a diagnosis of vulvar LC.

Conclusion: Vulvar lymphangioma may mimic other vulvar tumors. Excision may be the best treatment of extensive vulvar LC.

A case of lymphangioma circumscriptum with vulvar involvement is presented.

1Department of Gynecology and Obstetrics, Tehran University of Medical Sciences, Tehran; 2Gynecologic Oncology Department, Vali-e-Asr Hospital, Tehran; 3Department of Gynecology and Obstetrics, Shahid Sadoughi University of Medical Science, Yazd, Iran

Reprint requests to: Fatemeh Ghaemmaghami, MD, Gynecologic Oncology Department, Vali-e-Asr Hospital, Imam Khomeini Oncology Complex, Tehran 14194, Iran. E-mail:

©2007The American Society for Colposcopy and Cervical Pathology