Brief Clinical StudiesCombination of Sturge-Weber Syndrome and TrigonocephalyRistow, Oliver MD, DDS; Freudlsperger, Christian MD, DDS; Berger, Moritz MD, DDS; Bächli, Heidi MD; Hoffmann, Jürgen MD, DDS; Engel, Michael MD, DDSAuthor Information *Department of Oral and Maxillofacial Surgery †Department of Neurosurgery, University of Heidelberg, Im Neuenheimer Feld 400, Heidelberg, Germany. Address correspondence and reprint requests to PD Dr Dr Michael Engel, MD, DDS, Department of Oral and Maxillofacial Surgery, University of Heidelberg, Im Neuenheimer Feld 400, D-69120 Heidelberg, Germany; E-mail: email@example.com Received 17 May, 2016 Accepted 29 June, 2016 The authors report no conflicts of interest. Journal of Craniofacial Surgery: October 2016 - Volume 27 - Issue 7 - p e671-e673 doi: 10.1097/SCS.0000000000003055 Buy Metrics Abstract Regarded singly, both Sturge-Weber syndrome and trigonocephaly are rare congenital disorders. The cardinal features of Sturge-Weber syndrome are facial cutaneous capillary malformation (port-wine stain), leptomeningeal angiomatosis, and glaucoma. Premature closure of the metopic suture results in trigonocephaly. However, to the best of our knowledge, the diagnosis of a combination of both Sturge-Weber syndrome and trigonocephaly has not as yet been reported. This brief clinical study thus presents a patient with the unusual findings of a Sturge-Weber syndrome and simultaneous trigonocephaly induced by premature metopic synostosis. Thus, the rare combination of a port-wine stain involving the first division of the trigeminal nerve with the diagnosis of a craniosynostosis justifies the indication of a prophylactic magnetic resonance imaging acquisition before craniofacial surgeries, in order to prevent seizures and stroke-like episodes triggered by the surgical intervention. © 2016 by Mutaz B. Habal, MD.