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Isolated Unilateral Frontosphenoidal Craniosynostosis: A Rare Cause of Anterior Plagiocephaly

Pickrell, Brent B. MD*; Lam, Sandi K. MD; Monson, Laura A. MD*

doi: 10.1097/SCS.0000000000001950
Clinical Studies

Isolated unilateral frontosphenoidal synostosis is a rare and often misdiagnosed cause of synostotic frontal plagiocephaly. It is important to distinguish the various synostotic causes of frontal plagiocephaly from deformational frontal plagiocephaly because operative intervention is required in synostotic plagiocephaly to avoid progressive deformity, whereas deformational plagiocephaly typically improves without surgery. This study reports a patient with a unique case of anterior plagiocephaly caused by left-sided frontosphenoidal craniosynostosis. The workup should include a thorough history and clinical examination followed by computed tomography scan with three-dimensional reconstruction. Frontosphenoidal synostosis should be suspected in the absence of a coronal synostosis in a child with anterior unilateral plagiocephaly and treated surgically. Good aesthetic and functional results occur with prompt diagnosis and early surgical correction.

*Department of Surgery, Division of Plastic Surgery, Baylor College of Medicine, Houston, TX

Department of Surgery, Division of Neurosurgery, Baylor College of Medicine, Houston, TX.

Address correspondence and reprint requests to Laura A. Monson, MD, 6701 Fannin St. Suite 610.00, Houston, TX 77030; E-mail:

Received 25 February, 2015

Accepted 1 May, 2015

The authors report no conflicts of interest.

© 2015 by Mutaz B. Habal, MD.