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Imaging Findings of Klippel-Trenaunay Syndrome

Abdel Razek, Ahmed Abdel Khalek MD

Journal of Computer Assisted Tomography: September/October 2019 - Volume 43 - Issue 5 - p 786–792
doi: 10.1097/RCT.0000000000000895
Musculoskeletal Imaging
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We aim to review the imaging findings of Klippel-Trenaunay syndrome. This disorder characterized clinically by a triad of capillary malformations manifesting as a port-wine stain, venous varicosities typically along the lateral aspect of the lower extremities, and bone and/or soft tissue hypertrophy. Imaging of extremities shows unilateral venous varicosities, persistent embryonic veins, anomalous of the superficial and deep venous system, low-flow venolymphatic malformations, and bony and soft tissue hypertrophy. Other findings include neurospinal as cavernoma, aneurysm, and hemimegalencephaly, pulmonary as pulmonary thromboembolism and pulmonary hypertension and visceral as gastrointestinal and genitourinary vascular anomalies. Imaging may detect associated lesions and differentiate from simulating lesions.

From the Department of Diagnostic Radiology, Mansoura Faculty of Medicine, Mansoura University, Mansoura, Egypt.

Received for publication May 17, 2019; accepted May 21, 2019.

Correspondence to: Ahmed Abdel Khalek Abdel Razek, MD, Department of Diagnostic Radiology, Mansoura Faculty of Medicine, Elgomheryia St, Mansoura, Egypt 3512 (e-mail: arazek@mans.edu.eg).

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