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Computed Tomography Angiography and Magnetic Resonance Angiography of Congenital Anomalies of Pulmonary Veins

Abdel Razek, Ahmed Abdel Khalek, MD*; Al-Marsafawy, Hala, MD; Elmansy, Maha, MD*; El-Latif, Mahmoud Abd, MD*; Sobh, Donia, MD*

Journal of Computer Assisted Tomography: May/June 2019 - Volume 43 - Issue 3 - p 399–405
doi: 10.1097/RCT.0000000000000857
Cardiothoracic and Breast Imaging

We aimed to review computed tomography and magnetic resonance angiography of congenital anomalies of pulmonary veins. Total anomalous pulmonary venous return shows all pulmonary veins drain abnormally in another site rather than left atrium. Imaging can detect anomalous veins either supracardiac, infracardiac, or mixed. Partial anomalous pulmonary venous return shows some pulmonary vein have abnormal drainage that well delineated with computed tomography angiography. Scimitar syndrome is a type of partial anomalous pulmonary venous return where the pulmonary veins of the right lung drain infracardiac and is associated with right lung hypoplasia and dextrocardia. Pseudoscimitar show anomalous vein that takes a tortuous course and drains into the left atrium producing a false-positive scimitar sign. Cor triatriatum shows septum divide left atrium with proximal chamber receives blood flow from the pulmonary veins. Levoatriocardinal vein is an anomalous connection between the left atrium and anomalous vein from systemic venous system that is embryo logically derived from the cardinal veins. Computed tomography angiography can detect pulmonary vein stenosis, atresia, hypoplasia, and varix. Imaging is important for intimal diagnosis and detects the anomalous vessels and its connection, presence of stenosis, and associated other congenital cardiac anomalies. Also, it is a great role in assessment of patients after surgery.

From the *Department of Diagnostic Radiology and

Pediatric cardiology, Pediatric Hospital, Mansoura Faculty of Medicine, Mansoura, Egypt.

Received for publication January 24, 2019; accepted January 28, 2019.

Correspondence to: Ahmed Abdel Khalek Abdel Razek, MD, Department of Diagnostic Radiology, Mansoura Faculty of Medicine, 60 Elgomheryia St, Mansoura, Egypt 13351 (e-mail:

The authors declare no conflict of interest.

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