Amputation Versus Staged Reconstruction for Severe Fibular Hemimelia

Assessment of Psychosocial and Quality-of-Life Status and Physical Functioning in Childhood

Birch, John G., MD, FRCS(C)1; Paley, Dror, MD, FRCS(C)2; Herzenberg, John E., MD, FRCS(C)3; Morton, Anne, PhD1; Ward, Shana, PhD3; Riddle, Russ, MS1; Specht, Stacy, MPA3; Cummings, Don, CP1; Tulchin-Francis, Kirsten, PhD1

doi: 10.2106/JBJS.OA.18.00053
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Background: Fibular hemimelia, a congenital disorder characterized by the partial or complete absence of the fibula, tibial growth inhibition, and foot and ankle deformity and deficiency, is the most common deficiency of long bones. The purpose of the present study of children with congenital fibular hemimelia was to examine the functional and psychosocial outcomes at a minimum of 2 years after treatment either with amputation and a prosthesis or with reconstruction and lengthening.

Methods: Twenty children who were managed with primary amputation were compared with 22 children who were managed with staged limb reconstruction. The average age of the patients at the time of evaluation was 9 years (range, 5 to 15 years). Patients and parents completed psychosocial, quality-of-life, and satisfaction surveys. Patients underwent instrumented gait analysis and a timed 25 or 50-yard dash. The number and nature of surgical procedures were recorded from a retrospective chart review.

Results: Families of children managed with amputation had lower economic and educational levels and were more ethnically diverse compared with the families of children managed with limb reconstruction. Scores on psychosocial and quality-of-life surveys were comparable with those from healthy patient populations. Parents of males treated with amputation perceived a lower school-related quality of life for their child; socioeconomic and ethnic differences between groups might account for this finding. Statistically but not clinically significant differences were measured during instrumented gait analysis at a self-selected walking speed and during a timed 25 or 50-yard dash. The majority of patients and parents reported satisfaction with the treatment method selected and would select the same treatment method again.

Conclusions: At this interim stage of growth, there were no significant functional or psychological differences between groups. Both groups were satisfied with the outcome in mid-childhood, irrespective of the selection of amputation or limb reconstruction.

Level of Evidence: Therapeutic Level III. See Instructions for Authors for a complete description of levels of evidence.

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1Texas Scottish Rite Hospital for Children, Dallas, Texas

2Paley Orthopedic and Spine Institute, West Palm Beach, Florida

3The International Center for Limb Lengthening, Sinai Hospital of Baltimore, Baltimore, Maryland

E-mail address for D. Paley: dpaley@paleyinstitute.org

Investigation performed at Texas Scottish Rite Hospital for Children, Dallas, Texas, and the International Center for Limb Lengthening, Baltimore, Maryland

Disclosure: The authors indicated that no external funding was received for any aspect of this work. On the Disclosure of Potential Conflicts of Interest forms, which are provided with the online version of the article, one or more of the authors checked “yes” to indicate that the author had a relevant financial relationship in the biomedical arena outside the submitted work and “yes” to indicate that the author had other relationships or activities that could be perceived to influence, or have the potential to influence, what was written in this work (http://links.lww.com/JBJSOA/A91).

© 2019 The Authors. Published by Wolters Kluwer Health, Inc. on behalf of The Journal of Bone and Joint Surgery, Incorporated.