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A Rare Presentation and Management of Forearm Deformity in a Patient with Hereditary Multiple Exostoses

A Case Report

Agashe, Mandar, MS1,a; Shah, Avi, MS2; Parikh, Shital N., MD2

doi: 10.2106/JBJS.CC.17.00295
Case Reports
Disclosures

Case: We report the case of a patient with a long-standing and progressive forearm deformity, secondary to underlying hereditary multiple exostoses (HME). A salvage surgery was performed with excision of the pathologic parts of the radius and the ulna, followed by the creation of a 1-bone forearm.

Conclusion: One of the common manifestations of HME is forearm deformity due to abnormal ossification and osteochondromas that affect the radius and/or the ulna. Progressive deformity can lead to increasing pain, joint instability, limited motion, and functional decline. Neglected or recalcitrant deformities pose a treatment challenge. At 1.5 years after surgery, the patient had a satisfactory outcome with a fully functional, pain-free forearm in a fixed, neutral position.

1Center for Pediatric Orthopedic Care, Mumbai, India

2Cincinnati Children’s Hospital, Cincinnati, Ohio

aE-mail address for M. Agashe: mandarortho@gmail.com

Copyright © 2018 by The Journal of Bone and Joint Surgery, Incorporated
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