Kindler syndrome with unique ocular findings
A 40-year-old man presented with a 5-year history of diminution of vision. There was history of acral blisters in childhood and photosensitivity. The visual acuity was 20/400 in right eye and 20/120 in the left eye. Examination revealed conjunctivization of the cornea, lipidic degeneration at the limbus at 3 and 9 o' clock, and Salzmann nodular degeneration in both eyes. Mucocutaneous examination revealed cigarette paper like changes on the dorsum of hands and feet and poikilodermatous changes on photoexposed sites consistent with the diagnosis of Kindler syndrome [Fig. 1]. We report a case of Kindler syndrome with unique ocular manifestations.
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