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Concurrent solitary and multifocal congenital hypertrophy of the retinal pigment epithelium in a single eye

Gopal, Anand D; Kim, Jenna M; Shields, Carol L

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Indian Journal of Ophthalmology: July 2020 - Volume 68 - Issue 7 - p 1454
doi: 10.4103/ijo.IJO_2038_19
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A middle-aged Caucasian male was found to have pigmented fundus lesions in the left eye (OS). Visual acuity was 20/20 in both eyes. Funduscopic examination OS revealed a 10 mm × 10 mm flat, well-delineated, homogenously pigmented lesion consistent with solitary congenital hypertrophy of the retinal pigment epithelium (CHRPE, Fig. 1a black arrow). In addition, multifocal CHRPE, also known as bear tracks, were noted in the perimacular area [Fig. 1a white arrows]. All lesions demonstrated hypoautofluoresence [Fig. 1b]. The concurrence of solitary and multifocal CHRPE in one eye is rare. Gastrointestinal evaluation is not indicated for these lesions.[1]

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Figure 1:
Fundus photograph of the left eye demonstrates a 10 mm × 10 mm flat, well-delineated, homogenously pigmented lesion consistent with solitary congenital hypertrophy of the retinal pigment epithelium (CHRPE, a, black arrow). Multifocal CHRPE, also known as ”bear tracks,” are present in the perimacular area (a, white arrows). All lesions demonstrated hypoautofluorescence (b)

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Reference

1. Shields JA, Shields CL, Shah PG, Pastore DJ, Imperiale SM Jr. Lack of association among typical congenital hypertrophy of the retinal pigment epithelium, adenomatous polyposis, and Gardner syndrome Ophthalmology. 1992;99:1709–13
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