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Kindler syndrome with unique ocular findings

Thakur, Anchal; Kulshreshtha, Ashish; Kumar, Sheetanshu1; Dogra, Sunil1; Gupta, Amit

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Indian Journal of Ophthalmology: June 2020 - Volume 68 - Issue 6 - p 1182
doi: 10.4103/ijo.IJO_2261_19
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A 40-year-old man presented with a 5-year history of diminution of vision. There was history of acral blisters in childhood and photosensitivity. The visual acuity was 20/400 in right eye and 20/120 in the left eye. Examination revealed conjunctivization of the cornea, lipidic degeneration at the limbus at 3 and 9 o' clock, and Salzmann nodular degeneration in both eyes. Mucocutaneous examination revealed cigarette paper like changes on the dorsum of hands and feet and poikilodermatous changes on photoexposed sites consistent with the diagnosis of Kindler syndrome[12] [Fig. 1]. We report a case of Kindler syndrome with unique ocular manifestations.

Figure 1:
(a) Slit lamp photograph of the right eye showing mid-peripheral Salzmann nodular degeneration with conjunctivisation of the cornea with lipidic degeneration at the limbus. (b) Slit lamp photograph of the left eye showing central Salzmann nodular degeneration with conjunctivization of the cornea with lipidic degeneration at 4 and 8 o clock limbus. (c) Clinical photograph of the patient showing cigarette paper-like wrinkling of the dorsum of the hands and feet. (d) Clinical photograph of the extensor aspect of knee of the patient showing poikilodermatous changes

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The authors certify that they have obtained all appropriate patient consent forms. In the form the patient(s) has/have given his/her/their consent for his/her/their images and other clinical information to be reported in the journal. The patients understand that their names and initials will not be published and due efforts will be made to conceal their identity, but anonymity cannot be guaranteed.

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Conflicts of interest

There are no conflicts of interest.

1. Kindler T. Congenital poikiloderma with traumatic bulla formation and progressive cutaneous atrophy Br J Dermatol. 1954;66:104–11
2. Fischer IA, Kazandjieya J, Vassileva S, Dourmishev A. Kindler syndrome: A case report and proposal for clinical diagnostic criteria Acta Dermatovenerol Alp Pannonica Adriat. 2005;2:61–7
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