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Glaucoma in Phacomatosis Pigmentovascularis in a Young African Adolescent Boy

A Case Report

van der Merwe, Ernst B. MBChB, FCOphth(SA), MMed (Ophth); Bhika, Raquel E. MBChB; Meyer, David MBChB, FCFP (SA), MMed (Ophth), FCOphth(SA), PhD

doi: 10.1097/IJG.0000000000001264
Online Articles: Case Report/Small Case Series
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Background: Phacomatosis pigmentovascularis (PPV) has previously almost exclusively been reported in Asians and in dermatological journals. In this report, we present a case of a young black South African adolescent boy referred to our eye clinic.

Case Report: A 15-year-old male patient presented with gradual, painless loss of vision in his right eye. Clinical examination revealed a port-wine stain with ocular involvement on the right as well as a nevus of Ota. Fundoscopy on the right revealed an advanced glaucomatous optic disc and raised intraocular pressure. A diagnosis of glaucoma associated with PPV was made.

Conclusion: We present the first case of PPV in an African male individual with associated glaucoma seen at our tertiary hospital.

Division of Ophthalmology, Faculty of Medicine and Health Sciences, Tygerberg Academic Hospital and Stellenbosch University, Cape Town, South Africa

Disclosure: The authors declare no conflict of interest.

Reprints: Ernst B. van der Merwe, MBChB, FCOphth(SA), MMed (Ophth), Division of Ophthalmology, Faculty of Medicine and Health Sciences, Tygerberg Academic Hospital and Stellenbosch University, P.O. Box 241, Cape Town 8000, South Africa (e-mail: v_ernst_baard@hotmail.com).

Received November 16, 2018

Accepted April 6, 2019

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