Case ReportIridocorneal Endothelial Syndrome in a 16-Year-OldOlawoye, Olusola MD*; Teng, Christopher C. MD*,†,‡; Liebmann, Jeffrey M. MD*,‡; Wang, Frederick M. MD§; Ritch, Robert MD*,†Author Information *Einhorn Clinical Research Center, New York Eye and Ear Infirmary ‡Department of Ophthalmology, New York University School of Medicine, New York †Department of Ophthalmology, New York Medical College, Valhalla §Department of Ophthalmology, Albert Einstein College of Medicine, Bronx, NY Supported in part by the Albert Roubeni Fund of the New York Glaucoma Research Institute, New York, NY. Dr Olawoye was the recipient of a fellowship from the International Council of Ophthalmology, San Francisco, CA. Reprints: Christopher Teng, MD, Department of Ophthalmology, The New York Eye and Ear Infirmary, 310 East 14th Street, New York, NY 10003 (e-mail: [email protected]). Received January 22, 2010 Accepted April 25, 2010 Journal of Glaucoma: June/July 2011 - Volume 20 - Issue 5 - p 294-297 doi: 10.1097/IJG.0b013e3181e664b0 Buy Metrics Abstract We report iridocorneal endothelial syndrome in a male who presented at the age of 16 years with a 3-year history of complaints of blurred vision, altered pupillary shape, and monocular diplopia OD. The examination was notable for unilateral effacement of the iris architecture, stretch holes, corectopia, and localized ectropion uveae. Intraocular pressures were 41 mm Hg OD and 10 mm Hg OS. Gonioscopy revealed intermittent areas of broad synechiae anterior to Schwalbe's line alternating with a clinically normal appearance. The left eye and angle were unremarkable. Specular microscopy confirmed the presence of unilateral endothelial pleomorphism and polymegathism. To our knowledge, this is the earliest reported case of iridocorneal endothelial syndrome in a young man. © 2011 Lippincott Williams & Wilkins, Inc.