In Brief:
Idiopathic pulmonary hemosiderosis (IPH) is a rare condition, encountered mostly in children, and characterized by recurrent episodes of diffuse, bland alveolar hemorrhage of unclear etiology. With more sustained immunosuppressive therapy and possibly improved quality of care, the long-term outcome improved significantly, and consequently, more pediatric IPH cases are followed into adulthood. This entity needs to be differentiated from primary adult IPH, which is rare and, reportedly, more benign. This article presents an illustrative case of primary adult IPH and provides a review of epidemiology, pathogenesis, diagnosis and therapy for the disease.
