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Unilateral Multicystic Pulmonary Disease in a Young Adult

An Unusual Diagnosis

Goel, Ishan MD*; Kaushik, Parul MD; Xydis, Vassilis MD

Clinical Pulmonary Medicine: May 2019 - Volume 26 - Issue 3 - p 98–101
doi: 10.1097/CPM.0000000000000297
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Congenital pulmonary airway malformation (CPAM) is an uncommon developmental hamartomatous anomaly caused by abnormal branching of immature bronchioles with replacement of the lung by cysts/disorganized tissue. CPAMs are usually lobar or sublobar in extent, and ∼90% of lesions are identified within the first 2 years of life. CPAM occupying an entire lung, with a delayed adulthood presentation, is extremely rare; only 4 such occurrences have been previously described. We present a case of a 20-year-old woman diagnosed with unilateral entire lung CPAM on the basis of radiologic findings that was surgically resected via video-assisted thoracoscopic surgery.

Departments of *Radiodiagnosis

Anaesthesiology, Lady Hardinge Medical College, New Delhi, India

Department of Radiodiagnosis, University Hospital of Ioannina, Ioannina, Greece

Disclosure: The authors declare that they have no conflicts of interest.

Address correspondence to: Ishan Goel, MD, Department of Radiodiagnosis, Lady Hardinge Medical College, New Delhi 110001, India. E-mail: goel.ish06@gmail.com.

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