ColleaguesCongenital Pulmonary Airway MalformationWu, Zhi J. MD*; Narula, Navneet MD†; Beneck, Debra MD†; Nguyen, Andrew B. MD‡; Lee, Paul C. MD, MPH‡Author Information *Department of Cardiothoracic Surgery, New York Presbyterian/Queens, Flushing Departments of †Surgical Pathology ‡Cardiothoracic Surgery, Weill Cornell Medical Center, Weill Cornell Medical College, New York-Presbyterian Hospital, New York, NY Disclosure: The authors declare that they have no conflicts of interest. Address correspondence to: Paul C. Lee, MD, MPH, Weill Cornell Medical Center, New York-Presbyterian Hospital, 525 East 68th Street, P.O. Box 110, New York, NY 10065. E-mail: email@example.com. Clinical Pulmonary Medicine: September 2016 - Volume 23 - Issue 5 - p 227-230 doi: 10.1097/CPM.0000000000000168 Buy Metrics Abstract Congenital pulmonary airway malformation, previously known as congenital cystic adenomatoid malformation, is a rare congenital defect and is classified into 5 types. The exact mechanism is not well established, but studies have shown that bronchial atresia plays an important role in the pathogenesis. Molecular studies provided additional information about the disease. Most patients with congenital pulmonary airway malformation survive through pregnancy. Some of them present with respiratory distress after birth, with the rest remaining asymptomatic for years. The management of the asymptomatic patients is controversial. We present a review of the epidemiology, the pathophysiology, radiographic findings, treatment modalities, and recently published studies on the subject. Copyright © 2016 Wolters Kluwer Health, Inc. All rights reserved.