Invited Review ArticlesArrhythmogenic Right Ventricular Cardiomyopathy DiagnosisSayed, Amer MD; Pal, Suman MD; Poplawska, Maria MD; Aronow, Wilbert S. MD; Frishman, William H. MD; Fuisz, Anthon MD; Jacobson, Jason T. MDAuthor Information From the Department of Medicine, Cardiology Division, New York Medical College/Westchester Medical Center, Valhalla, NY. Disclosure: The authors have no conflicts of interest to report. Correspondence: Wilbert S. Aronow, MD, FACC, FAHA, Division of Cardiology, Westchester Medical Center and New York Medical College, Macy Pavilion, Room 141, 100 Woods Road, Valhalla, NY 10595. E-mail: firstname.lastname@example.org. Cardiology in Review: November/December 2020 - Volume 28 - Issue 6 - p 319-324 doi: 10.1097/CRD.0000000000000292 Buy Metrics Abstract Arrhythmogenic right ventricular cardiomyopathy, formerly called “arrhythmogenic right ventricular dysplasia,” is an under-recognized clinical entity characterized by ventricular arrhythmias and a characteristic ventricular pathology. Diagnosis is often difficult due to the nonspecific nature of the disease and the broad spectrum of phenotypic variations. Therefore, consensus diagnostic criteria have been developed which combine electrocardiographic, echocardiographic, cardiac magnetic resonance imaging and histologic criteria. In 1994, an international task force first proposed the major and minor diagnostic criteria of arrhythmogenic right ventricular cardiomyopathy based on family history, arrhythmias, electrocardiographic abnormalities, tissue characterization, and structural and functional right ventricular abnormalities. In 2010, the task force criteria were revised to include quantitative abnormalities. These diagnostic modalities and the most recent task force criteria are discussed in this review. Copyright © 2020 Wolters Kluwer Health, Inc. All rights reserved.