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Types of Tumors and Outcome of Treatment of 12 Patients With Nonmalignant Fibrosing Tumors in the Pediatric Hand

Baumholtz, Michael MD*; Netscher, David MD*; Popek, Edwina DO; Schneider, Adam M. MD*

doi: 10.1097/SAP.0b013e318160c13b
Hand Surgery and Microsurgery
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Nonmalignant fibrosing tumors in the pediatric hand or juvenile fibromatoses are uncommon and so may be a challenge to the clinician. We propose a diagnostic and treatment approach to nonmalignant fibrosing tumors of the pediatric hand based on a review of 12 patients who presented with 16 distinct hand lesions. We performed a retrospective 7-year chart review of 12 pediatric patients all with nonmalignant fibrosing conditions of the hand. All patients were operated on by a single surgeon (D.N.) and all samples were reviewed by a single pathologist (E.P.). Twenty-eight surgical procedures were performed on 12 patients. Lesions were classified by location (7 palmar, 9 dorsal) as well as clinicopathologic characteristics. It is imperative to have a broad differential when entertaining the diagnosis of juvenile fibromatosis. Most important, a diagnosis of true cancer must be ruled out. Other mimickers of this process (eg, juvenile rheumatoid arthritis) must also be considered. Most evaluations begin with magnetic resonance imaging and biopsy but a careful history is, as always, a key part of the evaluation. Some lesions may be observed once a diagnosis has been made. When surgical excision is indicated, wide resection is necessary. This may then require flap reconstruction with tendon and joint repair.

From the *Division of Plastic Surgery, Baylor College of Medicine, Houston, Texas; †Department of Pathology, Baylor College of Medicine, Texas Children's Hospital, Houston, Texas.

Received June 17, 2007 and accepted for publication, after revision, October 31, 2007.

Reprints: David Netscher, MD, 6624 Fannin, Suite 2730, Houston, TX 77030. E-mail: netscher@bcm.tmc.edu.

© 2008 Lippincott Williams & Wilkins, Inc.