CASE REPORTSChordoma Periphericum A Case ReportNielsen, G. Petur M.D.; Mangham, D. Chas. M.D.; Grimer, Robert J. M.D.; Rosenberg, Andrew E. M.D.Author Information From the James Homer Wright Pathology Laboratories, Massachusetts General Hospital, Harvard Medical School, Boston, Massachusetts, U.S.A. (G.P.N., A.E.R.), and the Department of Musculoskeletal Pathology, The Royal Orthopaedic Hospital, Birmingham, U.K. (D.C.M. and R.J.G.). Address correspondence and reprints requests to G. Petur Nielsen, MD, Department of Pathology, Massachusetts General Hospital, Fruit Street, Boston, MA 02114, U.S.A. The American Journal of Surgical Pathology: February 2001 - Volume 25 - Issue 2 - p 263-267 Buy Abstract The authors describe a tumor that had the histologic and ultrastructural features and immunohistochemical profile of an axial chordoma, but arose in the distal ulna. A skeletal survey failed to show any other site of involvement. The tumor was resected, and the patient remains free of disease 2½ years later. Rare tumors with the histologic features of chordoma have been reported in appendicular locations. Chordoma periphericum, a tumor that has the potential to metastasize, needs to be distinguished from parachordoma because no classic parachordoma has been reported to disseminate. © 2001 Lippincott Williams & Wilkins, Inc.