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Benefits of Maxillary Expansion for a Patient With Spinal Muscular Atrophy Type 2

Abeleira, María Teresa, DDS, PhD; Limeres, Jacobo, DDS, PhD; Outumuro, Mercedes, DDS, PhD; Vidal, Paula Sofía, DDS, MSc; Diniz-Freitas, Marcio, DDS, PhD; Ruíz-Piñón, Manuel, DDS, PhD; Diz Dios, Pedro, MD, DDS, PhD

American Journal of Physical Medicine & Rehabilitation: April 2019 - Volume 98 - Issue 4 - p e32–e34
doi: 10.1097/PHM.0000000000001022
Case Report

This case report involves a 10-yr-old boy diagnosed with spinal muscular atrophy type 2 who underwent nighttime mechanical ventilation with bilevel positive airway pressure. The oral examination revealed restricted mouth opening, lip interposition, dental crowding, and maxillary compression. After maxillary expansion, the upper airway volume increased 18.6%; 13 episodes of airway infections (20 days of hospitalization) were recorded in the 2 yrs before the maxillary expansion and only 4 episodes (no hospital admissions) in the 2 subsequent years. In conclusion, maxillary expansion in children with systemic disease that involves respiratory impairment may, in some cases, provide functional and clinical improvements, increase upper airway airflows, and possibly decrease the number of respiratory infections

From the Medical-Surgical Dentistry Research Group (OMEQUI), Health Research Institute of Santiago de Compostela (IDIS), University of Santiago de Compostela (USC), Santiago de Compostela, Spain (MTA, JL, MO, PSV, MD-F, PDD); and Operative Dentistry and Endodontics Unit, University of Santiago de Compostela, Santiago de Compostela, Spain (MR-P).

All correspondence should be addressed to: Pedro Diz Dios, MD, DDS, PhD, Special Needs Unit, School of Medicine and Dentistry, Santiago de Compostela University, 15782 Santiago de Compostela, Spain.

Details of this case report have not been previously presented.

Financial disclosure statements have been obtained, and no conflicts of interest have been reported by the authors or by any individuals in control of the content of this article.

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