Ventricular tachycardia (VT) storm, defined as recurrent VT requiring electrical cardioversion ≥3 times within 24 hours, is a rare presentation of long-QT syndrome. Pharmacologic autonomic modulation and/or left cardiac sympathetic denervation are established therapies in long-QT syndrome in adults but may not be effective or practical in the emergent treatment of VT storm. We present a novel case of a child with drug-refractory VT storm and prolonged QT requiring extracorporeal membrane oxygenation (ECMO) support. Continuous stellate ganglion blockade was remarkably effective in stabilizing his rhythm and should be considered in similar pediatric cases.
From the Departments of *Anesthesiology
†Pediatrics, Monroe Carell Jr. Children’s Hospital at Vanderbilt, Vanderbilt University Medical Center, Nashville, Tennessee.
Accepted for publication April 5, 2019.
The authors declare no conflicts of interest.
Address correspondence to Andrew D. Franklin, MD, MBA, Department of Anesthesiology, Monroe Carell Jr. Children’s Hospital at Vanderbilt, Vanderbilt University Medical Center, 2200 Children’s Way, Suite 3115, Nashville, TN 37232. Address e-mail to email@example.com.