Saul-Wilson syndrome, also known as microcephalic osteodysplastic dysplasia, is a rare type of dwarfism with significant anesthetic considerations. The genetic defect is associated with nearly uniform micrognathia, odontoid hypoplasia, and possible cervical spine instability that contribute to potentially increased risk of airway complications. Herein, we describe the anesthetic management of a 2-year-old child with Saul-Wilson syndrome.
From the University of Southern California, Los Angeles, California; and Department of Anesthesiology and Critical Care Medicine, Children’s Hospital Los Angeles, Los Angeles, California.
Accepted for publication February 8, 2019.
The authors declare no conflicts of interest.
Address correspondence to Marla M. Matar, MD, Department of Anesthesiology and Critical Care Medicine, Children’s Hospital Los Angeles, 4650 Sunset Blvd, Box 3, Los Angeles, CA 90027. Address e-mail to email@example.com.