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Anesthetic Challenges in an Adult with Mucopolysaccharidosis Type VI

Cade, Jacqueline MBBS, BMedSc; Jansen, Nicholas BSc, MBBS, FANZCA, PG Cert Emer Hlth

doi: 10.1213/XAA.0000000000000031
Case Reports: Case Report

The mucopolysaccharidoses are a group of lysosomal storage diseases with many skeletal and airway features that pose a challenge to anesthetists. We present the anesthetic management of a woman with mucopolysaccharidosis type VI undergoing cervical spine surgery and review the perioperative issues that may arise with this disease.

From the Department of Anesthesia, Royal Melbourne Hospital, Victoria, Australia.

Accepted for publication January 15, 2014.

Funding: None.

The authors declare no conflicts of interest.

Address correspondence to Jacqueline Cade, MBBS, BMedSc, Department of Anesthesia, Royal Melbourne Hospital, Grattan St, Parkville, 3050, Victoria, Australia. Address e-mail to

© 2014 International Anesthesia Research Society