Skip Navigation LinksHome > Summer 2014 - Volume 8 - Issue 3 > CENTRAL RETINAL ARTERY OCCLUSION AND SUSAC SYNDROME: A CASE...
RETINAL Cases & Brief Reports:
doi: 10.1097/ICB.0000000000000039
Case Report

CENTRAL RETINAL ARTERY OCCLUSION AND SUSAC SYNDROME: A CASE REPORT

Buelens, Tom MD*; Herode, Laurent MD*; Nubourgh, Isabelle MD; Caspers, Laure MD, PhD*; Willermain, François MD, PhD*; Postelmans, Laurence MD*

Collapse Box

Abstract

Background:

Susac syndrome is a rare disease attributed to microangiopathy involving the arterioles of the brain, retina, and cochlea. Understanding the pathogenesis is incomplete, but an immune-mediated process remains the leading hypothesis.

Methods:

Report of a single case of a previously healthy 22-year-old female patient showing the complete clinical triad.

Results:

Diagnosis of Susac syndrome in this patient was first questioned due to the atypical initial ophthalmologic presentation with central retinal artery occlusion. Multiple relapses occurred in the fellow eye during follow-up, showing the typical branch retinal artery occlusions, allowing definite diagnosis.

Conclusion:

Susac syndrome should be considered in the differential diagnosis when facing (young) patients with central retinal artery occlusion, especially in the presence of unexplained encephalopathy and/or sensorineural hearing loss.

Login

Search for Similar Articles
You may search for similar articles that contain these same keywords or you may modify the keyword list to augment your search.