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Vascularized Lymph Node Flap Transfer and Lymphovenous Anastomosis for Klippel-Trenaunay Syndrome with Congenital Lymphedema

Qiu, Shan Shan MD; Chen, Hsin-Yu MD; Cheng, Ming-Huei MD, MBA

Plastic and Reconstructive Surgery - Global Open: June 2014 - Volume 2 - Issue 6 - p e167
doi: 10.1097/GOX.0000000000000099
Case Reports
Taiwan

Summary: A female patient with Klippel-Trenaunay syndrome, including hypertrophic bone and soft tissue in the forelimbs, bilateral lower limbs lymphedema, port-wine stains, and superficial veins of Servelle, was presented. The diagnosis of lymphedema was confirmed by lymphoscintigraphy and indocyanine green lymphography. The novel treatments consisted of vascularized lymph node transplantation to the left lymphedematous extremity and lymphovenous anastomosis to the right lymphedematous extremity. Significant improvements in subjective and objective clinical outcome were observed early in the postoperative period with continued improvements during the follow-up period.

From the Division of Reconstructive Microsurgery, Department of Plastic and Reconstructive Surgery, Chang Gung Memorial Hospital, College of Medicine, Chang Gung University, Taoyuan, Taiwan.

Received for publication March 3, 2014; accepted March 25, 2014.

Disclosure: The authors have no financial interest to declare in relation to the content of this article. The Article Processing Charge was paid for by the authors.

Ming-Huei Cheng, MD, MBA, Division of Reconstructive Microsurgery, Department of Plastic and Reconstructive Surgery, Chang Gung Memorial Hospital, College of Medicine, Chang Gung University, 5, Fu-Hsing Street, Kweishan, Taoyuan 333, Taiwan, E-mail: minghuei@adm.cgmh.org.tw

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© 2014 American Society of Plastic Surgeons