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Correction of Angular Deformities Due to Focal Fibrocartilaginous Dysplasia Using Guided Growth: A Preliminary Report

Welborn, Michelle C. MD; Stevens, Peter MD

Journal of Pediatric Orthopaedics: April/May 2017 - Volume 37 - Issue 3 - p e183–e187
doi: 10.1097/BPO.0000000000000785
Lower Extremity

Background: Focal fibrocartilaginous dysplasia (FFCD) is a rare benign disorder that may result in tethering of the physis. These most commonly occur around the knee and may result in angular deformities of the involved extremity. To date treatment has ranged from observation, to curettage, to osteotomy. Our goal with this study is to evaluate the efficacy of guided growth in treating patients with angular deformity due to FFCD.

Methods: This is a retrospective review, we included 3 patients with angular deformities due to FFCD who had undergone 8 plate placement. We reviewed their preoperative and postoperative radiographs, assessed their sagittal and coronal balance and number of procedures.

Results: Three patients with FFCD of the femur with an average of 14 months underwent guided growth to correct their angular deformity. Once appropriate correction was achieved the hardware was removed. At final follow-up none of the patients required further surgical intervention for their angular deformity nor had they shown any evidence of recurrence.

Conclusions: FFCD is a rare benign disorder, they most commonly affects the proximal tibia and distal femur and can result in significant angular deformities. Our review of the literature found all of the cases involving the femur progressed to the point where they needed surgical intervention. This ranged from curettage to osteotomy. In this case series we present 3 cases of FFCD of the distal femur that were treated minimally invasively with guided growth.

Level of Evidence: Level 4.

*Shriners Hospital for Children, Portland, OR

University of Utah Primary Children’s Hospital, Salt Lake City, UT

Stevens P, receives royalties for their work with orthopediatrics, they did not receive any direct reimbursement for this study. There were no grants or outside funding associated with this study.

The authors declare no conflict of interest.

Reprints: Michelle C. Welborn, MD, Shriners Hospital for Children, 3101 SW Sam Jackson Park Road, Portland, OR 97239. E-mail: mwelborn@shrinenet.org.

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