We present a review of six cases of children with congenital pseudarthrosis of the clavicle, treated and followed up at the “La Fe” Hospital for Children. One of them had bilateral involvement. Five of them, including the bilateral case, were surgically treated at ages ranging from 18 months to 4 years. Bone graft and internal fixation with a Kirschner wire were used. Healing of the pseudarthrosis was obtained in all patients in 6–8 weeks. We discuss the suitability of early surgical treatment that, in our opinion, produces very satisfactory results.