Congenital penoscrotal lymphedema complicated by sepsis associated with a streptococcal infectionWATANABE, TORUPediatric Emergency Care: December 2000 - Volume 16 - Issue 6 - p 423-425 Illustrative Cases Abstract Author Information Congenital lymphedema is a relatively rare disease caused by congenital abnormality of the lymphatic system. Although bacterial infection frequently causes complications with lymphedema, severe sepsis in congenital lymphedema of the genitalia has not yet been reported. We describe a patient with congenital penoscrotal lymphedema complicated by cellulitis, lymphangitis, and severe sepsis associated with a streptococcal infection. This case represents the importance of obtaining a detailed clinical history and physical findings. From the Department of Pediatrics, Niigata City General Hospital, Niigata, Japan. Address for reprints: T. Watanabe, Department of Pediatrics, Niigata City General Hospital, 2–6-1 Shichikuyama, Niigata 950–8739, Japan; e-mail: email@example.com © 2000 Lippincott Williams & Wilkins, Inc.