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Dysplasia epiphysealis hemimelica of the elbow

Maalouf, Antoinea; Hage, Samer Ela; Haidar, Rachidb; Dagher, Fernanda; Kharrat, Khalila; Ghanem, Ismata

Journal of Pediatric Orthopaedics B:
doi: 10.1097/BPB.0b013e32833a5f8b
Upper Limb
Abstract

Dysplasia epiphysealis hemimelica (DEH) or Trevor's disease is a rare disorder affecting the epiphyses and short bones of the limbs, and characterized by a benign overgrowth of the medial-half of the epiphysis resembling osteochondroma. Upper limb involvement is very rare and most commonly affects the carpal bones. Only five established cases of DEH around the elbow were found in the orthopedic literature. We herein report an additional case of Trevor's disease of the elbow in a child with a symptomatic ulnar nerve compression and its management. To the best of our knowledge, this is the first case of DEH of the elbow presenting with nerve compromise.

Author Information

aDepartment of Orthopaedic Surgery, Hotel-Dieu de France Hospital, St Joseph University

bDepartment of Orthopaedic Surgery, American University of Beirut Medical Center, Beirut, Lebanon

Correspondence to Prof Ismat Ghanem, MD, Associate Professor of Orthopaedics, Pediatric Orthopaedic Surgery, Hôtel-Dieu de France Hospital, St Joseph University, Achrafieh, Beirut, Lebanon Tel: +961 1 615 300 x9112–9113; fax: +961 1 615 300 x9102; e-mail: ghanem.i@dm.net.lb

© 2011 Lippincott Williams & Wilkins, Inc.