Lymphomas predominantly affect the lymph nodes but can present at unusual sites, which are termed as extranodal lymphomas. Involvement of the ocular adnexa is an extremely uncommon occurrence, which is usually seen in patients with non-Hodgkin lymphoma. We report herewith an unusual case of a 5-year-old child with Hodgkin lymphoma and involvement of extraocular muscle leading to ptosis. The child was managed by alternating cycles of cyclophosphamide, vincristine, procarbazine and prednisolone and adriamycin, bleomycin, vinblastine, and dacarbazine. He had complete response to chemotherapy with resolution of ptosis.