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Journal of Pediatric Hematology/Oncology:
doi: 10.1097/MPH.0b013e318286d2ba
Online Articles: Clinical and Laboratory Observations

Neuroendocrine Tumor in Liver With Positive ACTH Receptor: A Case Report

Zein, Mohamad El MD; Vali, Reza MD; Charron, Martin MD; Manson, David MD; Perlman, Kusiel MD; Shammas, Amer MD

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Abstract

A rare case of possible primary ectopic adrenocorticotropic hormone (ACTH)-producing tumor in the liver mimicking a liver hemangioma is reported. A 9-year-old boy, with Cushing syndrome, was referred for the assessment of ectopic ACTH-producing tumor. Ultrasound, CT scan, and MRI of the abdomen revealed a liver lesion suggestive of a hemangioma. 111In-octreotide scintigraphy revealed focal activity in the liver, indicative of a somatostatin-positive lesion. 99mTc-labeled RBC scintigraphy was negative for hemangioma. After surgical resection of the tumor, the cortisol level converted to a normal range indicative of a rare possible primary ACTH-producing tumor in the liver, which was confirmed by histopathology.

© 2014 by Lippincott Williams & Wilkins.

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