Skip Navigation LinksHome > July 2013 - Volume 35 - Issue 5 > Clear Cell Sarcoma of the Jaw: A Case Report and Review of t...
Journal of Pediatric Hematology/Oncology:
doi: 10.1097/MPH.0b013e3182580d1f
Clinical and Laboratory Observations

Clear Cell Sarcoma of the Jaw: A Case Report and Review of the Literature

Inoue, Susumu MD*,†; Chepeha, Douglas B. MD, MSPH; Lucas, David R. MD§,∥; Faisal, Shahzad MD; Stewart, Ronald C. DDS#; Mushtaq, Rao MD; Onwuzurike, Nkechi MD*,†; McQuillan, Lori MSHE**

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Abstract

Clear cell sarcoma (CSS) is a unique malignant soft tissue tumor that mainly occurs from the aponeurotic tissue and tendons of extremities. It is rare in the pediatric population. The tumor does not respond well to chemotherapy or irradiation. Complete surgical resection offers the best chance for a cure. Most studies have demonstrated poor prognosis of this tumor, if it is >5 cm. The literature suggests that local recurrence and distant metastasis are not uncommon even with wide resection and that late recurrence and metastasis commonly occur. This case report discusses CSS in the jaw of a pediatric patient. To our knowledge, this is the only case of CSS of the jaw.

Copyright © 2012 by Lippincott Williams & Wilkins

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