Background: Endometriosis is a common disease of unclear etiology found in women of reproductive age. Symptoms of endometriosis usually resolve in the absence of normal ovarian function but have been reported to recur in the presence of hormone replacement.
Case: We report a case of endometriosis in a patient with Turner syndrome who presented with abdominal pain and a pelvic mass. She underwent exploratory laparotomy, total abdominal hysterectomy, and excision of her ovary. The pelvic mass was consistent with cystic endometriosis. Her postoperative course was complicated by the diagnosis of aberrantly left-sided superior vena cava and moderate lupus anticoagulant.
Conclusion: The incidence of endometriomas in patients with Turner syndrome on hormone replacement therapy is unknown but should be considered in the differential diagnosis of pelvic pain in these patients.