Osteolipomas of the head and neck are very rare, and there is no reported case of osteolipoma of the nasopharynx in the literature. Here, we present a case of osteolipoma of the nasopharynx in a 21-year-old male who was referred for a nasopharyngeal mass causing a defect in the left half of the soft palate. The well-demarcated, firm tumor was excised through transnasal endoscopic and transpalatal approaches, and the defect of the soft palate was repaired by a superiorly based pharyngeal flap. Osteolipomas should be kept in mind in the differential diagnosis of nasopharyngeal mass as an extremely rare benign lesion.