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Sturge-Weber Syndrome and Associated Congenital Vascular Disorders: A Review

Nathan, Nirmal BS*; Thaller, Seth R. MD, DMD

Journal of Craniofacial Surgery: July 2006 - Volume 17 - Issue 4 - pp 724-728
Special Section: Vascular Anomalies

Sturge-Weber syndrome (SWS), Klippel-Trenaunay syndrome (KTS), and Parkes-Weber syndrome (PWS) represent a wide range of congenital vascular abnormality syndromes. Although many of the diagnostic criteria overlap for these syndromes, there are important differences among these diseases that carry important prognostic and therapeutic implications. This review attempts to clearly distinguish among SWS, KTS, and PWS, although loosely categorizing them as a family of congenital vascular disorders. A review of literature reveals that a variety of diagnostic tools exist that can help differentiate between the syndromes and assess risk for certain complications, which may help tailor various treatment modalities for a particular patient.

From the *Miller School of Medicine at the University of Miami, Miami, Florida; and the Division of Plastic and Reconstructive Surgery, Miller School of Medicine at the University of Miami, Miami, Florida.

Miami, Florida, USA

Address correspondence and reprint requests to Nirmal Nathan, BS, Miller School of Medicine at the University of Miami, 808 Brickell Key Drive #806, Miami, FL 33131; E-mail: n.nathan@umiami.edu

© 2006 Mutaz B. Habal, MD