Skip Navigation LinksHome > February 2014 - Volume 123 - Issue 2, PART 2 > Gynecologic and Surgical Complications in Type IV Ehlers-Dan...
Obstetrics & Gynecology:
doi: 10.1097/AOG.0000000000000001
Case Report

Gynecologic and Surgical Complications in Type IV Ehlers-Danlos Syndrome

Wheeler, Sarahn M. MD; Russo, Melissa MD; Wilson-Murphy, Molly; Shen, Wen MD

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BACKGROUND: Although type IV Ehlers-Danlos syndrome is a rare condition, it is critical that physicians be aware of this disease because it presents unique management challenges.

CASE: We present a young woman who was admitted with a pelvic abscess after having a miscarriage and an appendiceal perforation. She had an exploratory laparotomy secondary to a persistent pelvic abscess and endured multiple postoperative complications. Based on her family history and physical characteristics, type IV Ehlers-Danlos syndrome was diagnosed.

CONCLUSION: The decision to proceed with surgery should be weighed against tissue fragility in patients with type IV Ehlers-Danlos syndrome. A conservative, multidisciplinary team approach addresses whether to proceed with surgery and minimize postoperative complications if surgery is performed.

© 2014 by The American College of Obstetricians and Gynecologists.


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