Paradoxical Myotonia in Paramyotonia Congenita
Video demonstrates the characteristic paradoxical increase in myotonia with repetitive hand grips, or paramyotonia, seen in patients with paramyotonia congenita. The patient is instructed to squeeze her hand closed as tightly as she can and then open her hand quickly. This maneuver is repeated to evaluate forwarm-up of myotonia or paradoxical worsening.
Richard J. Barohn, MD, FAAN
CONTINUUM: Lifelong Learning in Neurology. 19(6, Muscle Disease):1598-1614, December 2013