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Mounier-Kuhn Syndrome

Simon, Marioara PhD; Vremaroiu, Petrut MD; Andrei, Fabian MD

Journal of Bronchology & Interventional Pulmonology: April 2014 - Volume 21 - Issue 2 - p 145–149
doi: 10.1097/LBR.0000000000000068
Bronchoscopic Images

Mounier-Kuhn syndrome or congenital tracheobronchomegaly is a rare clinical and radiologic condition. It is characterized by a tracheal and bronchial dilation. Fewer than 100 cases have been reported in the medical literature since the original description in 1932. The first utilization of bronchoscopy for diagnosis of this condition was recorded by Lemoine only in 1949. The cause of this condition is not clearly understood; however, histopathologic findings of atrophy of smooth muscles and elastic tissue in the trachea and main bronchi have been observed. Tracheobronchomegaly can be associated with tracheal and bronchial diverticuli.

Pneumology Hospital “Leon Daniello” Cluj-Napoca, Romania

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Disclosure: There is no conflict of interest or other disclosures.

Reprints: Marioara Simon, PhD, 36 Densusianu street, Cluj-Napoca, cod 400428, Romania (e-mail: masiroro@yahoo.com).

Received June 8, 2013

Accepted March 3, 2014

© 2014 by Lippincott Williams & Wilkins.