Skip Navigation LinksHome > September 2013 - Volume 34 - Issue 3 > Sudden Death and Isolated Right Ventricular Noncompaction Ca...
American Journal of Forensic Medicine & Pathology:
doi: 10.1097/PAF.0b013e3182a0a46c
Case Reports

Sudden Death and Isolated Right Ventricular Noncompaction Cardiomyopathy: Report of 2 Autopsied Adult Cases

Ilyas, Sadaf MD*; Ganote, Charles MD*; Lajoie, Dawn MD; Robertson, Julie MD; Cline-Parhamovich, Karen DO

Collapse Box

Abstract

A predominantly right ventricular variant of isolated noncompaction cardiomyopathy is a potentially lethal disease entity, which only recently has become recognized in the clinical and cardiac imaging literature. There are currently few established morphologic criteria for the diagnosis other than right ventricular dilation and presence of excessive regional trabeculation. To date, there have been no autopsy reports of cases following either clinical diagnosis or sudden death. We report 2 adult cases of sudden unexpected death in which unexplained right ventricular dilation and prominent apical hypertrabeculation were the principal findings. The gross and microscopic results suggest pathological similarities between, or coexistence of, right ventricular noncompaction and arrhythmogenic right ventricular cardiomyopathies.

Copyright © 2013 by Lippincott Williams & Wilkins

Login

Article Tools

Share

Search for Similar Articles
You may search for similar articles that contain these same keywords or you may modify the keyword list to augment your search.