Abstract: Self-healing juvenile cutaneous mucinosis (SHJCM) is a rare disorder of unknown origin, which occurs in children in good health. It is characterized by the multiplication of transient cutaneous papules and nodules, mainly located on the head and periarticular areas that spontaneously resolve. Histological features of SHJCM have been well described; therefore, the diagnosis is usually made easily when papules are biopsied. We report a series of 3 new cases of SHJCM presenting mainly with nodular lesions. Histological examination of these nodules showed either lesions consistent with nodular or proliferative fasciitis or nonspecific panniculitis. Mucinous deposits were present but often inconspicuous, so could be disregarded. We wanted to emphasize this misleading presentation because a biopsy for histological examination is always mandatory in cases of proliferating nodules to rule out malignant tumors. Therefore, the diagnosis always requires discussion between pathologists and clinicians to rapidly reassure the parents and avoid inappropriate therapy.
*Department of Dermatology , Centre Hospitalier Universitaire de Caen, Université de Caen Basse-Normandie, UFR de Médecine, Caen, France
†Université libanaise, Beyrouth, Liban
‡National Pathology Institut, Université Libanaise, Beyrouth, Liban
§Department of Dermatology, Centre Hospitalier du Nord, Zgharta, Liban
¶Department of Dermatology, Hôpital St-Joseph, Marseille, France
‖Department of Dermatology, Centre Hospitalier St-Martin, Caen, France
**Department of Orthopaedics
††Department of Anatomo-pathology, Centre Hospitalier Universitaire de Caen, Université de Caen Basse-Normandie, UFR de Médecine, Caen, France
‡‡Department of Anatomo-pathology, Hôpital Necker-Enfants Malades, APHP, Université Paris-Descartes, Paris, France.
Reprints: Sylvie Fraitag, MD, Department of Anatomo-pathology, Hôpital Necker Enfants Malades, 149 Rue de Sèvres, Paris 75743, France (e-mail: firstname.lastname@example.org).
The authors declare no conflicts of interest.