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Giant, Congenital Folliculosebaceous Cystic Hamartoma: A Case Against a Pathogenetic Relationship With Trichofolliculoma

Cole, Patrick MD*; Kaufman, Yoav MD*; Dishop, Megan MD†; Hatef, Daniel A MD*; Hollier, Larry MD*

American Journal of Dermatopathology: October 2008 - Volume 30 - Issue 5 - pp 500-503
doi: 10.1097/DAD.0b013e318183eb07
Brief Report

Folliculosebaceous cystic hamartoma (FSCH) is a rare cutaneous hamartoma consisting of dilated folliculosebaceous units invested in mesenchymal elements. These solitary lesions typically affect adults, have a predilection for the central face or scalp, and remain less than 1.5 cm in greatest dimension. Although giant FSCH variants have been documented, the congenital presentation of a giant FSCH stands in contrast to earlier views of its histogenetic relationship with trichofolliculoma. We describe a giant pedunculated FSCH arising from the posterior neck of a 9-month-old Hispanic male and discuss various aspects of this highly unusual case.

From the Departments of *Plastic Surgery; and †Pathology, Baylor College of Medicine, Houston, TX.

Reprints: Dr. Patrick Cole, MD, Department of Plastic Surgery, Baylor College of Medicine, 6701 Fannin, Houston, TX 77030 (e-mail: pdcole@bcm.tmc.edu).

© 2008 Lippincott Williams & Wilkins, Inc.